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Sodhi, Rakhee, Khanduri, Sushant, Jethani, Varuna, Nadia, Shirazi, Kumar, Manoj. (1396). An Unusual Presentation of Granulomatosis with Polyangiitis. , 5(3), 204-207. doi: 10.22038/jctm.2017.24298.1135
Rakhee Sodhi; Sushant Khanduri; Varuna Jethani; Shirazi Nadia; Manoj Kumar. "An Unusual Presentation of Granulomatosis with Polyangiitis". , 5, 3, 1396, 204-207. doi: 10.22038/jctm.2017.24298.1135
Sodhi, Rakhee, Khanduri, Sushant, Jethani, Varuna, Nadia, Shirazi, Kumar, Manoj. (1396). 'An Unusual Presentation of Granulomatosis with Polyangiitis', , 5(3), pp. 204-207. doi: 10.22038/jctm.2017.24298.1135
Sodhi, Rakhee, Khanduri, Sushant, Jethani, Varuna, Nadia, Shirazi, Kumar, Manoj. An Unusual Presentation of Granulomatosis with Polyangiitis. , 1396; 5(3): 204-207. doi: 10.22038/jctm.2017.24298.1135

An Unusual Presentation of Granulomatosis with Polyangiitis

Journal of Cardio-Thoracic Medicine
مقاله 8، دوره 5، شماره 3، آذر 2017، صفحه 204-207    اصل مقاله (1005.76 K)
نوع مقاله: Case Report
شناسه دیجیتال (DOI): 10.22038/jctm.2017.24298.1135
نویسندگان
Rakhee Sodhi* 1؛ Sushant Khanduri2؛ Varuna Jethani3؛ Shirazi Nadia4؛ Manoj Kumar5
1Internal Medicine, Pulmonologist, Department of Pulmonary Medicine, Himalayan Institute of Medical Sciences, Dehradun,Indian
2Critical Care Medicine, Department of Critical Care Medicine, Himalayan Insitute of Medical Sciences, Dehradu, Indian
3Senior Resident, Department of Pulmonary Medicine, Himalayan Institute of Medical Sciences, Dehradun, Indian
4Pathologist, Department of Pathology, Himalayan Institute of Medical Sciences, Dehradun, Indian
5Resident, Department of Pulmonary Medicine, Himalayan Institute of Medical Sciences, Dehradun, Indian
چکیده
The granulomatosis with polyangiitis (GPA), formerly known as Wegener’s granulomatosis, is a pauci-immune vasculitis involving small- and medium-sized blood vessels. Classically, the patients inflicted with this disease present with a triad of necrotizing granulomatous inflammation of the respiratory tract, cutaneous necrotizing vasculitis, and glomerulonephritis (GN).
The antinuclear (ANA) and anti-neutrophil cytoplasmic antibodies (ANCA) are considered as relatively specific markers of the disease. Herein, we presented the case of a patient who initially presented with sepsis but did not respond to the conventional antibiotics and later diagnosed with GPA.The granulomatosis with polyangiitis (GPA), formerly known as Wegener’s granulomatosis, is a pauci-immune vasculitis involving small- and medium-sized blood vessels. Classically, the patients inflicted with this disease present with a triad of necrotizing granulomatous inflammation of the respiratory tract, cutaneous necrotizing vasculitis, and glomerulonephritis (GN).
The antinuclear (ANA) and anti-neutrophil cytoplasmic antibodies (ANCA) are considered as relatively specific markers of the disease. Herein, we presented the case of a patient who initially presented with sepsis but did not respond to the conventional antibiotics and later diagnosed with GPA.
کلیدواژه‌ها
Antinuclear antibody؛ Anti-neutrophil cytoplasmic antibody؛ Granulomatosis With Polyangiitis؛ Sepsis
مراجع
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