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Fallahi, Minoo, Alaei, Fariba, Khalilian, Mohammad Reza, Alaei, Mastaneh, Vahidshahi, Kourosh, Ansari, Faezeh, Nilipour, Yalda. (1400). Congenital Heart Defects in Hirschsprung's Disease: A Survey in Iranian Population. , 13(1), 36-39. doi: 10.22038/ijn.2021.57874.2088
Minoo Fallahi; Fariba Alaei; Mohammad Reza Khalilian; Mastaneh Alaei; Kourosh Vahidshahi; Faezeh Ansari; Yalda Nilipour. "Congenital Heart Defects in Hirschsprung's Disease: A Survey in Iranian Population". , 13, 1, 1400, 36-39. doi: 10.22038/ijn.2021.57874.2088
Fallahi, Minoo, Alaei, Fariba, Khalilian, Mohammad Reza, Alaei, Mastaneh, Vahidshahi, Kourosh, Ansari, Faezeh, Nilipour, Yalda. (1400). 'Congenital Heart Defects in Hirschsprung's Disease: A Survey in Iranian Population', , 13(1), pp. 36-39. doi: 10.22038/ijn.2021.57874.2088
Fallahi, Minoo, Alaei, Fariba, Khalilian, Mohammad Reza, Alaei, Mastaneh, Vahidshahi, Kourosh, Ansari, Faezeh, Nilipour, Yalda. Congenital Heart Defects in Hirschsprung's Disease: A Survey in Iranian Population. , 1400; 13(1): 36-39. doi: 10.22038/ijn.2021.57874.2088

Congenital Heart Defects in Hirschsprung's Disease: A Survey in Iranian Population

Iranian Journal of Neonatology
دوره 13، شماره 1، فروردین 2022، صفحه 36-39    اصل مقاله (726.51 K)
نوع مقاله: Original Article
شناسه دیجیتال (DOI): 10.22038/ijn.2021.57874.2088
نویسندگان
Minoo Fallahi1؛ Fariba Alaei* 2؛ Mohammad Reza Khalilian3؛ Mastaneh Alaei4؛ Kourosh Vahidshahi3؛ Faezeh Ansari5؛ Yalda Nilipour6
1Neonatal Health Research Center, Research Institute for Children's Health, Shahid Beheshti University of Medical Sciences, Tehran, Iran
2Pediatric Cardiology Department, Mofid Children's Hospital, Faculty of Medicine, Shahid Beheshti University of Medical Sciences, Tehran, Iran
3Pediatric Cardiology Department, Shahid Modarres Hospital, Faculty of Medicine, Shahid Beheshti University of Medical Sciences, Tehran, Iran
4Blood Transfusion Research Center, High Institute for Research and Education in Transfusion Medicine, Tehran, Iran
5Mofid Children's Hospital, Faculty of Medicine, Shahid Beheshti University of Medical Sciences, Tehran, Iran
6Pediatric Pathology Research Center, Research Institute for Children's Health, Shahid Beheshti University of Medical Sciences, Tehran, Iran
چکیده
Background: Hirschsprung's disease (HSCR) may be accompanied by other anomalies, including congenital heart disease (CHD), resulting in additional complications. This study was performed to evaluate the prevalence and type of concomitant CHD in hospitalized children with HSCR.
Methods: All HSCR patients (n=129) admitted to Mofid Children's Hospital in Tehran, Iran, from April 2016 to August 2019 were investigated in a descriptive cross-sectional study. Two-dimensional, M-mode and pulsed, continuous, and color Doppler provided echocardiography were applied to evaluate cardiac structure and function.
Results: CHD was observed in 48 (37.2%) cases, and the most common anomalies were Atrial Septal Defect (ASD) in 20 (15.5%), Ventricular Septal Defect (VSD) in 1 (0.8%), Patent Ductus Arteriosus (PDA) in 2 (1.6%), Tetralogy of Fallot in 3 (2.3%), ASD and Pulmonary stenosis in 2 (1.6%), ASD and PDA in 7 (5.4%), ASD and VSD in 3 (2.3%), as well as VSD and PDA in 2 (1.6%) patients.
Conclusion: Cardiac anomalies are relatively prevalent in the Iranian HSCR population participating in the present study. In addition, early echocardiographic evaluation in the setting of HSCR is recommended.
 
 
کلیدواژه‌ها
Congenital anomaly؛ Congenital heart disease؛ Hirschsprung's disease
مراجع
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