The Complication of Endotracheal Intubation in a Patient with Mucopolysaccharidosis Type IIIA | ||
International Journal of Pediatrics | ||
مقاله 1، دوره 9، شماره 2 - شماره پیاپی 86، اردیبهشت 2021، صفحه 12909-12913 اصل مقاله (428.08 K) | ||
شناسه دیجیتال (DOI): 10.22038/ijp.2020.47300.3837 | ||
نویسندگان | ||
Dilber Ademhan Tural* 1؛ Nagehan Emiralioglu2؛ Beste Ozsezen2؛ Kismet Cıkı3؛ Nursun Ozcan4؛ Burak Ardicli5؛ Serap Sivri3 | ||
1Department of Pediatric Pulmonology, Ihsan Dogramaci Children’s Hospital, Hacettepe University Faculty of Medicine, Ankara, Turkey. | ||
2Department of Pediatric Pulmonology, Ihsan Dogramaci Children’s Hospital, Hacettepe University Faculty of Medicine, Ankara, Turkey. | ||
3Department of Pediatric Metabolism, Ihsan Dogramaci Children’s Hospital, Hacettepe University Faculty of Medicine, Ankara, Turkey. | ||
4Department of Radiology, Hacettepe University Faculty of Medicine, Ankara, Turkey. | ||
5Department of Pediatric Surgery, Hacettepe University Faculty of Medicine, Ankara, Turkey | ||
چکیده | ||
Mucopolysaccharidosis type III (MPS III), also known as Sanfilippo syndrome, is an autosomal recessive, neurodegenerative lysosomal storage disorder. Substantial challenges for airway management and endotracheal intubation are predictable due to the MPS patients' specific phenotypic, facial, and airway characteristics. In studies concerning various types of MPS, the incidence of difficult endotracheal intubation ranges between 28%-44%. This study intends to present a case with MPSIIIA, who aspirated her tooth during endotracheal intubation due to acute respiratory failure. This study reports a 12.5 year-old girl who presented with MPSIIIA and aspirated her tooth during endotracheal intubation due to acute respiratory failure resulting in lung lobe segmentectomy. The majority of MPS patients’ intubation and airway maintenance are hard and get even more difficult by age because of their mental retardation and oral health deteriorating, which may require tracheostomy. | ||
کلیدواژهها | ||
Aspiration؛ Child؛ Difficult Airway Maintenance؛ Intubation؛ MPS Type IIIA | ||
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