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Vargas, David, Sandoval, Jose Antonio, Castillo, Luz Dinora, Sánchez, Sandra, Uribe, Eduardo, Arizmendi, Alejandro, Aguilar, Francisco, Aceves, José. (1399). Arrhythmogenic right ventricular cardiomyopathy a diagnostic challenge in young: A case report. , 8(4), 727-729. doi: 10.22038/jctm.2020.53135.1302
David Vargas; Jose Antonio Sandoval; Luz Dinora Castillo; Sandra Sánchez; Eduardo Uribe; Alejandro Arizmendi; Francisco Aguilar; José Luis Aceves. "Arrhythmogenic right ventricular cardiomyopathy a diagnostic challenge in young: A case report". , 8, 4, 1399, 727-729. doi: 10.22038/jctm.2020.53135.1302
Vargas, David, Sandoval, Jose Antonio, Castillo, Luz Dinora, Sánchez, Sandra, Uribe, Eduardo, Arizmendi, Alejandro, Aguilar, Francisco, Aceves, José. (1399). 'Arrhythmogenic right ventricular cardiomyopathy a diagnostic challenge in young: A case report', , 8(4), pp. 727-729. doi: 10.22038/jctm.2020.53135.1302
Vargas, David, Sandoval, Jose Antonio, Castillo, Luz Dinora, Sánchez, Sandra, Uribe, Eduardo, Arizmendi, Alejandro, Aguilar, Francisco, Aceves, José. Arrhythmogenic right ventricular cardiomyopathy a diagnostic challenge in young: A case report. , 1399; 8(4): 727-729. doi: 10.22038/jctm.2020.53135.1302

Arrhythmogenic right ventricular cardiomyopathy a diagnostic challenge in young: A case report

Journal of Cardio-Thoracic Medicine
مقاله 7، دوره 8، شماره 4، اسفند 2020، صفحه 727-729    اصل مقاله (202.24 K)
نوع مقاله: Case Report
شناسه دیجیتال (DOI): 10.22038/jctm.2020.53135.1302
نویسندگان
David Vargas1؛ Jose Antonio Sandoval1؛ Luz Dinora Castillo1؛ Sandra Sánchez2؛ Eduardo Uribe1؛ Alejandro Arizmendi2؛ Francisco Aguilar1؛ José Luis Aceves* 1
1Pediatric Cardiology Department. NMC 20 de Noviembre ISSSTE. México City.
2Pediatric Cardiology department NMC 20 de Noviembre ISSSTE
چکیده
Clinical presentation of Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) usually is nonspecific in young, representing a challenge diagnostic. We present an 11-year-old male patient, with a syncope event and normal ECG in the first medical assessment. Eight months later, presented a new syncope event, but now with 1st degree block that evolved to complete AV block in 24 hrs in ECG. In Tertiary Medical Care Hospital showed sinus arrhythmia with nodal rescues. The echocardiographic assessment showed dilatation and global hypokinesia in the Right Ventricle.  The MR showed in apex and lateral wall late Gadolinium enhancement indicating fibrosis greater than 20%. The electrophysiologic assessment showed a low-voltage zone in the RVOT, normal stimulation between sinus and AV nodes. Was implanted ICD which identified events of ventricular tachycardia (185 bpm), giving discharges between 21 to 41 Jules, which were not perceived for the patient. Currently continues under cardiology surveillance to eventually receive a heart transplant as definitive treatment
کلیدواژه‌ها
Right Ventricular؛ Cardiomyopathy؛ Uhl´s Disease
مراجع
References

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آمار
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