Hemophilic Pseudotumors: Diagnosis and Management | ||
The Archives of Bone and Joint Surgery | ||
مقاله 1، دوره 8، شماره 2، خرداد 2020، صفحه 121-130 اصل مقاله (1.67 M) | ||
نوع مقاله: CURRENT CONCEPTS REVIEW | ||
شناسه دیجیتال (DOI): 10.22038/abjs.2019.40547.2090 | ||
نویسنده | ||
E. Carlos RODRIGUEZ-MERCHAN* | ||
Department of Orthopaedic Surgery, La Paz University Hospital, Madrid, Spain | ||
چکیده | ||
Prevention is essential for avoiding the complications of muscle hematomas (pseudotumors, compartment syndromes and peripheral nerve lesions) in hemophilic patients. This is achieved through early diagnosis of muscle hematomas and proper long-term hematological treatment until they have resolved (confirmed by image studies). Ultrasound-guided percutaneous drainage could be beneficial in terms of achieving better and faster symptom relief. When suspecting a hemophilic pseudotumor, biopsy will help us confirm the diagnosis and rule out true tumors (chondrosarcoma, liposarcoma, synovial sarcoma) that sometimes mimic hemophilic pseudotumor. Surgical removal of hemophilic pseudotumor is the best solution. As alternatives, there are curettage and filling with cancellous bone and radiotherapy (when surgery is contraindicated). Preoperative arterial embolization (ideally 2 weeks before surgery) helps control intraoperative bleeding during surgery for giant pelvic pseudotumors. Level of evidence: III | ||
کلیدواژهها | ||
Hemophilia؛ Muscle hematomas؛ Prevention؛ Pseudotumors؛ Treatment | ||
مراجع | ||
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